ICD-11 code : XH1ZH1;
Preferred Label : Pineoblastoma;
ICD-11 definition : Pineoblastomas are a rare, malignant type of supratentorial primitive neuroectodermal
tumor, found mainly in children (less than 10% of cases are reported in adults), located
in the pineal region of the brain but that can metastasize along the neuroaxis. As
they are the most aggressive of the pineal parenchymal tumors, they are usually associated
with a poor prognosis.;
Origin ID : 1679690951;
Automatic exact mappings (from CISMeF team)
Pineoblastomas are a rare, malignant type of supratentorial primitive neuroectodermal
tumor, found mainly in children (less than 10% of cases are reported in adults), located
in the pineal region of the brain but that can metastasize along the neuroaxis. As
they are the most aggressive of the pineal parenchymal tumors, they are usually associated
with a poor prognosis.