ICD-11 code : GB81;
Preferred Label : Autosomal dominant polycystic kidney disease;
ICD-11 definition : Multiple cysts in both kidneys increasing in number and size from adolescence, associated
with development of hypertension and chronic renal failure. Autosomal dominant familial
pattern is usual and due to mutations on Chromosomes 16 and 4. Non-renal manifestations
can include cysts in the liver and less commonly pancreas,. Cerebral arterial aneurysms
with subarachnoid haemorrhage, and other non-renal vascular abnormalities can also
occur.;
ICD-11 synonym : APCKD - [autosomal polycystic kidney disease]; adult polycystic kidney disease; Polycystic kidney, adult type; autosomal polycystic kidney disease;
ICD-11 acronym : APCKD;
Origin ID : 91220434;
Currated CISMeF NLP mapping
ICD-10 Mapping
Multiple cysts in both kidneys increasing in number and size from adolescence, associated
with development of hypertension and chronic renal failure. Autosomal dominant familial
pattern is usual and due to mutations on Chromosomes 16 and 4. Non-renal manifestations
can include cysts in the liver and less commonly pancreas,. Cerebral arterial aneurysms
with subarachnoid haemorrhage, and other non-renal vascular abnormalities can also
occur.