ICD-11 definition : Lymphangioleiomyomatosis (LAM) is a multiple cystic lung disease characterized by
progressive cystic destruction of the lung and lymphatic abnormalities, frequently
associated with renal angiomyolipomas (AMLs). LAM occurs either sporadically or as
a manifestation of tuberous sclerosis complex (TSC, ).;
Lymphangioleiomyomatosis (LAM) is a multiple cystic lung disease characterized by
progressive cystic destruction of the lung and lymphatic abnormalities, frequently
associated with renal angiomyolipomas (AMLs). LAM occurs either sporadically or as
a manifestation of tuberous sclerosis complex (TSC, ).