ICD-11 code : KA88;
Preferred Label : Disseminated intravascular coagulation of fetus or newborn;
ICD-11 definition : Neonatal purpura fulminans is a potentially lethal disorder characterised by progressive
haemorrhagic necrosis of the skin associated with cutaneous vascular thrombosis. It
is usually due to a genetically transmitted thrombophilic disorder: most commonly
homozygous deficiency of protein C or, less frequently, protein S.;
ICD-11 inclusion : Neonatal purpura fulminans;
Origin ID : 742410330;
Currated CISMeF NLP mapping
- ICD-10 Mapping
Neonatal purpura fulminans is a potentially lethal disorder characterised by progressive
haemorrhagic necrosis of the skin associated with cutaneous vascular thrombosis. It
is usually due to a genetically transmitted thrombophilic disorder: most commonly
homozygous deficiency of protein C or, less frequently, protein S.
