ICD-11 code : 7A21;
Preferred Label : Idiopathic hypersomnia;
ICD-11 definition : Idiopathic hypersomnia is characterised by daily periods of irrepressible need to
sleep or daytime lapses into sleep occurring for at least several months in the absence
of cataplexy or hypocretin deficiency (if determined). Polysomnography/multiple sleep
latency test (MSLT) findings characteristic of narcolepsy (i.e., two or more sleep-onset
REM periods (SOREMP's), or one or more SOREMP's on MSLT and a SOREMP on the preceding
overnight polysomnography) should also be absent. The daytime sleepiness is not better
explained by another disorder (e.g., insufficient sleep syndrome, obstructive sleep
apnoea, circadian rhythm sleep-wake disorder), a substance or medication, or a medical
condition). Objective evidence of hypersomnolence is indicated by an MSLT showing
a mean sleep latency of 8 minutes or by polysomnography or wrist actigraphy showing
a total 24-hour sleep time of 11 hours or more. Prolonged and severe sleep inertia
is often observed and consists of sustained difficulty waking up with repeated returns
to sleep, irritability, automatic behaviour, and confusion. In contrast to narcolepsy,
naps are generally long, often more than 60 minutes, and unrefreshing. Note: A definitive
diagnosis requires daily periods of irrepressible need to sleep or daytime lapses
into sleep, objective demonstration of excessive sleepiness and absence of REM-related
findings by multiple sleep latency test (MSLT/PSG).;
ICD-11 synonym : disorder of excessive somnolence; excessive somnolence; hypersomnia;
Origin ID : 631826564;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
See also inter- (CISMeF)
Idiopathic hypersomnia is characterised by daily periods of irrepressible need to
sleep or daytime lapses into sleep occurring for at least several months in the absence
of cataplexy or hypocretin deficiency (if determined). Polysomnography/multiple sleep
latency test (MSLT) findings characteristic of narcolepsy (i.e., two or more sleep-onset
REM periods (SOREMP's), or one or more SOREMP's on MSLT and a SOREMP on the preceding
overnight polysomnography) should also be absent. The daytime sleepiness is not better
explained by another disorder (e.g., insufficient sleep syndrome, obstructive sleep
apnoea, circadian rhythm sleep-wake disorder), a substance or medication, or a medical
condition). Objective evidence of hypersomnolence is indicated by an MSLT showing
a mean sleep latency of 8 minutes or by polysomnography or wrist actigraphy showing
a total 24-hour sleep time of 11 hours or more. Prolonged and severe sleep inertia
is often observed and consists of sustained difficulty waking up with repeated returns
to sleep, irritability, automatic behaviour, and confusion. In contrast to narcolepsy,
naps are generally long, often more than 60 minutes, and unrefreshing. Note: A definitive
diagnosis requires daily periods of irrepressible need to sleep or daytime lapses
into sleep, objective demonstration of excessive sleepiness and absence of REM-related
findings by multiple sleep latency test (MSLT/PSG).