ICD-11 code : MF85;
Preferred Label : Anti-glomerular basement membrane antibody mediated disease;
ICD-11 definition : Anti-GBM mediated glomerulonephritis is an aggressive focal and segmental proliferative
glomerular disease characterised by linear staining of the glomerular basement membrane
for immunoglobulins, particularly IgG and IgM. Crescentic change is often associated
and circulating anti-bodies to glomerular basement membrane are found in active disease.
The renal syndrome is often acute nephritis with rapid renal functional decline (rapidly
progressive nephritis) and if associated with respiratory involvement (haemoptyiss,
respiratory failure) the couple is termed is Goodpastures syndrome;
ICD-11 synonym : Goodpasture syndrome; Anti-glomerular basement membrane antibody disease;
ICD-11 inclusion : Goodpasture syndrome;
Origin ID : 591736785;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
Anti-GBM mediated glomerulonephritis is an aggressive focal and segmental proliferative
glomerular disease characterised by linear staining of the glomerular basement membrane
for immunoglobulins, particularly IgG and IgM. Crescentic change is often associated
and circulating anti-bodies to glomerular basement membrane are found in active disease.
The renal syndrome is often acute nephritis with rapid renal functional decline (rapidly
progressive nephritis) and if associated with respiratory involvement (haemoptyiss,
respiratory failure) the couple is termed is Goodpastures syndrome