ICD-11 code : 4A44;
Preferred Label : Vasculitis;
ICD-11 definition : Vasculitides represent a heterogenous group of diseases of multifactorial aetiology
characterized by inflammatory lesions of vessels. These lesions consist of fibrinoid
necrosis (necrotizing arteritis), giant cell infiltration without necrosis, immunoglobulins
deposit or leukocytoclastic infiltration. The spectrum and severity of the systemic
vaculitides is broad, from life or sight threatening fulminant disease to relatively
minor skin disease.;
ICD-11 "other" category code : 4A44.Y;
ICD-11 "unspecified" category code : 4A44.Z;
Origin ID : 572581721;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
Vasculitides represent a heterogenous group of diseases of multifactorial aetiology
characterized by inflammatory lesions of vessels. These lesions consist of fibrinoid
necrosis (necrotizing arteritis), giant cell infiltration without necrosis, immunoglobulins
deposit or leukocytoclastic infiltration. The spectrum and severity of the systemic
vaculitides is broad, from life or sight threatening fulminant disease to relatively
minor skin disease.