ICD-11 code : LA89;
Preferred Label : Functionally univentricular heart;
ICD-11 definition : The term functionally univentricular heart describes a spectrum of congenital cardiovascular
malformations in which the ventricular mass may not readily lend itself to partitioning
that commits one ventricular pump to the systemic circulation, and another to the
pulmonary circulation. Additional information: a heart may be functionally univentricular
because of its anatomy or because of the lack of feasibility or lack of advisability
of surgically partitioning the ventricular mass. Common lesions in this category typically
include double inlet right ventricle (DIRV), double inlet left ventricle (DILV), tricuspid
atresia, mitral atresia, and hypoplastic left heart syndrome. Other lesions which
sometimes may be considered to be a functionally univentricular heart include complex
forms of atrioventricular septal defect, double outlet right ventricle, congenitally
corrected transposition, pulmonary atresia with intact ventricular septum, and other
cardiovascular malformations. Specific diagnostic codes should be used whenever possible,
and not the term functionally univentricular heart.;
ICD-11 synonym : univentricular heart; Single ventricle; Univentricular cardiopathy;
ICD-11 inclusion : Common ventricle; Absence of ventricular septum; Absence of interventricular septum; Agenesis of ventricular septum;
ICD-11 "other" category code : LA89.Y;
ICD-11 "unspecified" category code : LA89.Z;
Origin ID : 5417233;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
The term functionally univentricular heart describes a spectrum of congenital cardiovascular
malformations in which the ventricular mass may not readily lend itself to partitioning
that commits one ventricular pump to the systemic circulation, and another to the
pulmonary circulation. Additional information: a heart may be functionally univentricular
because of its anatomy or because of the lack of feasibility or lack of advisability
of surgically partitioning the ventricular mass. Common lesions in this category typically
include double inlet right ventricle (DIRV), double inlet left ventricle (DILV), tricuspid
atresia, mitral atresia, and hypoplastic left heart syndrome. Other lesions which
sometimes may be considered to be a functionally univentricular heart include complex
forms of atrioventricular septal defect, double outlet right ventricle, congenitally
corrected transposition, pulmonary atresia with intact ventricular septum, and other
cardiovascular malformations. Specific diagnostic codes should be used whenever possible,
and not the term functionally univentricular heart.
