ICD-11 code : LA89;
Preferred Label : Functionally univentricular heart;
ICD-11 definition : The term functionally univentricular heart describes a spectrum of congenital cardiovascular
malformations in which the ventricular mass may not readily lend itself to partitioning
that commits one ventricular pump to the systemic circulation, and another to the
pulmonary circulation. A heart may be functionally univentricular because of its anatomy
or because of the lack of feasibility or lack of advisability of surgically partitioning
the ventricular mass. Common lesions in this category typically include double inlet
right ventricle (DIRV), double inlet left ventricle (DILV), tricuspid atresia, mitral
atresia, and hypoplastic left heart syndrome. Other lesions which sometimes may be
considered to be a functionally univentricular heart include complex forms of atrioventricular
septal defect, double outlet right ventricle, congenitally corrected transposition,
pulmonary atresia with intact ventricular septum, and other cardiovascular malformations.
Specific diagnostic codes should be used whenever possible, and not the term functionally
univentricular heart. Specific diagnostic codes whenever possible instead of the term
functionally univentricular heart.;
ICD-11 synonym : univentricular heart; Single ventricle; Univentricular cardiopathy;
ICD-11 inclusion : Common ventricle; Absence of ventricular septum; Absence of interventricular septum; Agenesis of ventricular septum;
ICD-11 "other" category code : LA89.Y;
ICD-11 "unspecified" category code : LA89.Z;
Origin ID : 5417233;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
The term functionally univentricular heart describes a spectrum of congenital cardiovascular
malformations in which the ventricular mass may not readily lend itself to partitioning
that commits one ventricular pump to the systemic circulation, and another to the
pulmonary circulation. A heart may be functionally univentricular because of its anatomy
or because of the lack of feasibility or lack of advisability of surgically partitioning
the ventricular mass. Common lesions in this category typically include double inlet
right ventricle (DIRV), double inlet left ventricle (DILV), tricuspid atresia, mitral
atresia, and hypoplastic left heart syndrome. Other lesions which sometimes may be
considered to be a functionally univentricular heart include complex forms of atrioventricular
septal defect, double outlet right ventricle, congenitally corrected transposition,
pulmonary atresia with intact ventricular septum, and other cardiovascular malformations.
Specific diagnostic codes should be used whenever possible, and not the term functionally
univentricular heart. Specific diagnostic codes whenever possible instead of the term
functionally univentricular heart.
