ICD-11 code : DC33;
Preferred Label : Autoimmune pancreatitis;
ICD-11 definition : Autoimmune pancreatitis (AIP) is a rare pancreatic disease characterized by chronic
non-alcoholic pancreatitis that presents with abdominal pain, steatorrhoea, obstructive
jaundice and responds well to steroid therapy and is seen in two subforms: type 1
AIP which affects elderly males, involves other organs and has increased immunoglobin
G4 (IgG4) levels and type 2 AIP which affects both sexes equally but presents at a
younger age and has no other organ involvement or increased IgG4 levels.;
Origin ID : 2057951941;
Currated CISMeF NLP mapping
ICD-10 Mapping
Autoimmune pancreatitis (AIP) is a rare pancreatic disease characterized by chronic
non-alcoholic pancreatitis that presents with abdominal pain, steatorrhoea, obstructive
jaundice and responds well to steroid therapy and is seen in two subforms: type 1
AIP which affects elderly males, involves other organs and has increased immunoglobin
G4 (IgG4) levels and type 2 AIP which affects both sexes equally but presents at a
younger age and has no other organ involvement or increased IgG4 levels.