ICD-11 code : LA03;
Preferred Label : Arnold-Chiari malformation type II;
ICD-11 definition : A condition caused by failure of the brain and spinal cord to correctly develop during
the antenatal period. This condition is characterized by extension of both cerebellar
and brain stem tissue into the foramen magnum. This condition may present with partial
or complete absence of the cerebellar vermis, myelomeningocele, neck pain, balance
problems, muscle weakness, limb numbness, dizziness, vision problems, difficulty swallowing,
ringing in the ears, hearing loss, vomiting, insomnia, depression, or impairment of
motor skills.;
ICD-11 synonym : Arnold-Chiari syndrome NOS; Arnold-Chiari obstruction type II; Chiari malformation type II; Arnold-Chiari malformation NOS;
Origin ID : 1987349422;
UMLS CUI : C0555206;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
- Semantic type(s)
- UMLS correspondences (same concept)
- Validated automatic mappings to NTBT
A condition caused by failure of the brain and spinal cord to correctly develop during
the antenatal period. This condition is characterized by extension of both cerebellar
and brain stem tissue into the foramen magnum. This condition may present with partial
or complete absence of the cerebellar vermis, myelomeningocele, neck pain, balance
problems, muscle weakness, limb numbness, dizziness, vision problems, difficulty swallowing,
ringing in the ears, hearing loss, vomiting, insomnia, depression, or impairment of
motor skills.
