" /> Immunodeficiency-associated lymphoproliferative disorders - CISMeF





ICD-11 code : 2B32;

Preferred Label : Immunodeficiency-associated lymphoproliferative disorders;

ICD-11 definition : Post-transplant lymphoproliferative disorder (PTLD) is a polyclonal (benign) or clonal (malignant) proliferation of lymphoid cells that develops as a consequence of immunosuppression in a recipient of a solid organ or bone marrow allograft. PTLDs comprise a spectrum ranging from early, Epstein-Barr virus (EBV)-driven polyclonal lymphoid proliferations to EBV-positive or EBV- negative lymphomas of predominantly B-cell or less often T-cell type. In other Immunodeficiency-associated lymphoproliferative disorders, association with EBV is less pronounced.;

ICD-11 synonym : Post transplant lymphoproliferative disorder; PTLD - [Post transplant lymphoproliferative disorder];

ICD-11 acronym : PTLD;

ICD-11 inclusion : PTLD - [Post transplant lymphoproliferative disorder];

ICD-11 "other" category code : 2B32.Y;

ICD-11 "unspecified" category code : 2B32.Z;

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Post-transplant lymphoproliferative disorder (PTLD) is a polyclonal (benign) or clonal (malignant) proliferation of lymphoid cells that develops as a consequence of immunosuppression in a recipient of a solid organ or bone marrow allograft. PTLDs comprise a spectrum ranging from early, Epstein-Barr virus (EBV)-driven polyclonal lymphoid proliferations to EBV-positive or EBV- negative lymphomas of predominantly B-cell or less often T-cell type. In other Immunodeficiency-associated lymphoproliferative disorders, association with EBV is less pronounced.

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19/05/2024


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