ICD-11 code : 4A62;
Preferred Label : Behçet disease;
ICD-11 definition : Behçet disease is a disease of incompletely understood aetiopathogenesis characterized
by recurrent oral and/or genital aphthous ulcers accompanied by cutaneous, ocular,
articular, gastrointestinal, and/or central nervous system inflammatory lesions. Small
vessel vasculitis, thrombotic vasculopathy, arteritis and arterial aneurysms may occur.
It has a high prevalence from the Eastern Mediterranean across Central Asia to China
and Japan.;
ICD-11 synonym : Adamantiades-Behçet disease;
ICD-11 inclusion : Adamantiades-Behçet disease;
Origin ID : 1668927157;
UMLS CUI : C0004943;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Semantic type(s)
UMLS correspondences (same concept)
Behçet disease is a disease of incompletely understood aetiopathogenesis characterized
by recurrent oral and/or genital aphthous ulcers accompanied by cutaneous, ocular,
articular, gastrointestinal, and/or central nervous system inflammatory lesions. Small
vessel vasculitis, thrombotic vasculopathy, arteritis and arterial aneurysms may occur.
It has a high prevalence from the Eastern Mediterranean across Central Asia to China
and Japan.