ICD-11 code : 2B52;
Preferred Label : Ewing sarcoma, primary site;
ICD-11 definition : A small round cell tumor that lacks morphologic, immunohistochemical, and electron
microscopic evidence of neuroectodermal differentiation. It represents one of the
two ends of the spectrum called Ewing's sarcoma/peripheral neuroectodermal tumor.
It affects mostly males under age 20, and it can occur in soft tissue or bone. Pain
and the presence of a mass are the most common clinical symptoms.;
ICD-11 synonym : Ewing's sarcoma/PNET; Ewing tumour of unspecified site;
ICD-11 "other" category code : 2B52.Y;
ICD-11 "unspecified" category code : 2B52.Z;
Origin ID : 1651102476;
Automatic exact mappings (from CISMeF team)
A small round cell tumor that lacks morphologic, immunohistochemical, and electron
microscopic evidence of neuroectodermal differentiation. It represents one of the
two ends of the spectrum called Ewing's sarcoma/peripheral neuroectodermal tumor.
It affects mostly males under age 20, and it can occur in soft tissue or bone. Pain
and the presence of a mass are the most common clinical symptoms.
