ICD-11 code : 4A60;
Preferred Label : Monogenic autoinflammatory syndromes;
ICD-11 definition : Monogenic hereditary autoinflammatory diseases characterized by apparently unprovoked
generalized inflammation in the absence of infection or high titre autoantibodies.;
ICD-11 "other" category code : 4A60.Y;
ICD-11 "unspecified" category code : 4A60.Z;
Origin ID : 1576710885;
Currated CISMeF NLP mapping
ICD-10 Mapping
Validated automatic mappings to NTBT
Monogenic hereditary autoinflammatory diseases characterized by apparently unprovoked
generalized inflammation in the absence of infection or high titre autoantibodies.