ICD-11 code : 8E00;
Preferred Label : Sporadic Creutzfeldt-Jakob Disease;
ICD-11 definition : A disease of the brain, that is associated with a mutation of normal prion protein
genes or spontaneous transformation of prion proteins. This disease is characterized
by a long incubation period, progressive dementia, neurological deficits, and is fatal.
Transmission may be by direct contact with infected nervous tissue or blood. Confirmation
is by pathological examination of the brain.;
ICD-11 synonym : Creutzfeld-Jakob disease NOS; idiopathic Creutzfeldt-Jakob disease; sCJD - [Sporadic Creutzfeldt-Jakob Disease]; sCJD;
Origin ID : 1553463690;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
A disease of the brain, that is associated with a mutation of normal prion protein
genes or spontaneous transformation of prion proteins. This disease is characterized
by a long incubation period, progressive dementia, neurological deficits, and is fatal.
Transmission may be by direct contact with infected nervous tissue or blood. Confirmation
is by pathological examination of the brain.