ICD-11 code : 2C70;
Preferred Label : Malignant neoplasms of vulva;
ICD-11 definition : Squamous cell carcinoma of the vulva occurs predominantly in the older age group.
Although the incidence rate of vulvar intraepithelial neoplasia is increasing, that
of squamous cell carcinoma of the vulva is declining, reflecting earlier detection
and more successful treatment. In addition to human papillomavirus infection, cigarette
smoking is a putative risk factor for vulvar squamous cell carcinoma. There are three
known precursor lesions: vulvar intraepithelial neoplasia, lichen sclerosis and chronic
granulomatous disease. Other important epithelial malignancies of the vulva are Paget
disease and Bartholin gland carcinoma. They are much less common than squamous lesions,
and the risk factors are largely unknown. Prominent non-epithelial tumours are malignant
melanoma and sarcoma botyoides.;
ICD-11 synonym : vulvar carcinoma; cancer of vulva; vulval cancer; malignant tumor of vulva;
ICD-11 "other" category code : 2C70.Y;
ICD-11 "unspecified" category code : 2C70.Z;
Origin ID : 1530443809;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Validated automatic mappings to BTNT
Squamous cell carcinoma of the vulva occurs predominantly in the older age group.
Although the incidence rate of vulvar intraepithelial neoplasia is increasing, that
of squamous cell carcinoma of the vulva is declining, reflecting earlier detection
and more successful treatment. In addition to human papillomavirus infection, cigarette
smoking is a putative risk factor for vulvar squamous cell carcinoma. There are three
known precursor lesions: vulvar intraepithelial neoplasia, lichen sclerosis and chronic
granulomatous disease. Other important epithelial malignancies of the vulva are Paget
disease and Bartholin gland carcinoma. They are much less common than squamous lesions,
and the risk factors are largely unknown. Prominent non-epithelial tumours are malignant
melanoma and sarcoma botyoides.