" /> Junctional epidermolysis bullosa - CISMeF





ICD-11 code : EC31;

Preferred Label : Junctional epidermolysis bullosa;

ICD-11 definition : Junctional (lucidolytic) epidermolysis bullosa is due to defects at the level of the lamina lucida of the epidermal basement membrane. The generalised severe form (Herlitz) is associated with widespread mucosal involvement of internal organs and has a high mortality in infancy.;

ICD-11 synonym : Junctional EB; JEB - [junctional epidermolysis bullosa]; Lucidolytic epidermolysis bullosa; Junctional EB - [epidermolysis bullosa]; epidermolysis bullosa;

ICD-11 acronym : JEB;

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Junctional (lucidolytic) epidermolysis bullosa is due to defects at the level of the lamina lucida of the epidermal basement membrane. The generalised severe form (Herlitz) is associated with widespread mucosal involvement of internal organs and has a high mortality in infancy.

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10/05/2025


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