ICD-11 code : CB03;
Preferred Label : Idiopathic interstitial pneumonitis;
ICD-11 definition : The idiopathic interstitial pneumonias (pneumonitises) are a subset of diffuse interstitial
lung diseases of unknown etiology characterized by expansion of the interstitial compartment
(i.e. that portion of the lung parenchyma sandwiched between the epithelial and endothelial
basement membranes) with an infiltrate of inflammatory cells. The inflammatory infiltrate
is sometimes accompanied by fibrosis, either in the form of abnormal collagen deposition
or proliferation of fibroblasts capable of collagen synthesis.;
ICD-11 synonym : interstitial pneumonia NOS; Idiopathic interstitial pneumonia; nonspecific interstitial pneumonitis;
ICD-11 inclusion : Idiopathic interstitial pneumonia;
ICD-11 "other" category code : CB03.Y;
ICD-11 "unspecified" category code : CB03.Z;
Origin ID : 1297512293;
Automatic exact mappings (from CISMeF team)
ICD-10 Mapping
The idiopathic interstitial pneumonias (pneumonitises) are a subset of diffuse interstitial
lung diseases of unknown etiology characterized by expansion of the interstitial compartment
(i.e. that portion of the lung parenchyma sandwiched between the epithelial and endothelial
basement membranes) with an infiltrate of inflammatory cells. The inflammatory infiltrate
is sometimes accompanied by fibrosis, either in the form of abnormal collagen deposition
or proliferation of fibroblasts capable of collagen synthesis.