ICD-11 code : CB06;
Preferred Label : Pulmonary alveolar microlithiasis;
ICD-11 definition : Pulmonary alveolar microlithiasis is an idiopathic rare disease in which concretions
composed of calcium and phosphorus collect in alveolar spaces. A systemic disorder
of calcium metabolism has not been identified, and the serum calcium and phosphate
levels are normal. Cough and dyspnea are the most common presenting symptoms. Expectorated
microliths have been reported. Inspiratory crackles, finger clubbing, and signs of
cor pulmonale may be present in more advanced disease.;
Origin ID : 1220010076;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
Pulmonary alveolar microlithiasis is an idiopathic rare disease in which concretions
composed of calcium and phosphorus collect in alveolar spaces. A systemic disorder
of calcium metabolism has not been identified, and the serum calcium and phosphate
levels are normal. Cough and dyspnea are the most common presenting symptoms. Expectorated
microliths have been reported. Inspiratory crackles, finger clubbing, and signs of
cor pulmonale may be present in more advanced disease.
