ICD-11 code : 4A42;
Preferred Label : Systemic sclerosis;
ICD-11 definition : Systemic sclerosis is a systemic disorder of the connective tissue; manifested by
hardening and thickening of the skin, by abnormalities involving the microvasculature
and larger vessels, and by fibrotic degenerative changes in various body organs including
the heart, lungs, kidneys, and gastrointestinal tract. (Arthritis Rheum 1980;23:581-590);
ICD-11 synonym : Systemic scleroderma; progressive scleroderma;
ICD-11 inclusion : Systemic scleroderma;
ICD-11 "unspecified" category code : 4A42.Z;
Origin ID : 1084365812;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Systemic sclerosis is a systemic disorder of the connective tissue; manifested by
hardening and thickening of the skin, by abnormalities involving the microvasculature
and larger vessels, and by fibrotic degenerative changes in various body organs including
the heart, lungs, kidneys, and gastrointestinal tract. (Arthritis Rheum 1980;23:581-590)